Oral findings in Coffin-Siris syndrome: A case report

نویسندگان

چکیده

This paper reports the oral health approach of a child with Coffin-Siris syndrome. syndrome is multisystem congenital anomaly caused by mutations in genes BRG-1-associated factors complex. Individuals this have been described hypoplasia or aplasia fifth digit nails phalanges. Other features include growth deficiency, developmental and intellectual delay, other organ-system abnormalities. Clinical examination revealed gingival hyperplasia upper arch, dental biofilm, caries on lower deciduous permanent molars. Guidelines hygiene dietary habits were provided to guardians, tooth extraction restoration glass-ionomer cement performed. case suggests that these patients require home care periodic consultations for preventive systematic treatment quality life improvement. The patient being monitored, her condition has improved.

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ژورنال

عنوان ژورنال: Revista Portuguesa de Estomatologia, Medicina Dentária e Cirurgia Maxilofacial

سال: 2021

ISSN: ['1646-2890', '1647-6700']

DOI: https://doi.org/10.24873/j.rpemd.2021.03.826